IgG4-related sclerosing cholangitis: liver biopsy findings
نویسندگان
چکیده
IgG4-related autoimmune disease is a recently recognized clinical entity associated with autoimmune pancreatitis, various systemic extrapancreatic lesions and an elevated serum IgG4 level. IgG4-related sclerosing cholangitis (IgG4-SC) is one of the extrapancreatic manifestations of this entity, which needs to be differentiated from primary sclerosing cholangitis (PSC) as these two diseases appear similar at presentation, but follow different clinical courses. In this issue, we will discuss the histopathologic findings of IgG4-SC based on a liver biopsy case of a 65-year-old patient with autoimmune pancreatitis.
منابع مشابه
Extensive Metastatic Cholangiocarcinoma Associated With IgG4-Related Sclerosing Cholangitis Misdiagnosed as Isolated IgG4-Related Sclerosing Cholangitis
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